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Abstract
Hirschsprung's disease is a congenital disorder, characterized by the absence of cells of the enteric nervous system in the most distal part of the intestine, the most frequent clinical manifestation of which is the delay in the exit of meconium. There are several forms of presentation of the disease, the most frequent being the rectosigmoid variant. The clinical history, physical examination, contrast enema, and abdominal radiography are useful to guide the diagnostic suspicion, but the definitive diagnosis is made by taking adequate biopsies. The treatment of the disease without association of complications is mainly surgical and the technique of choice will depend on the form of the disease.
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References
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