Resumen
El síndrome de Prune Belly o síndrome de Eagle Barret es una malformación congénita rara de etiología desconocida, caracterizada por la triada: hipoplasia de la pared muscular abdominal, criptorquidia y anomalías del tracto urinario. El cuadro clínico que desencadena es variable, dependiendo sobre todo del grado de alteración del sistema urinario y compromiso renal. La detección del síndrome de Prune Belly, en su mayoría, se realiza ya sea por medio de ultrasonografía antenatal o en el periodo neonatal. Su tratamiento suele ser conservador, con excepciones donde es necesaria la intervención quirúrgica, la cual depende de la gravedad de los síntomas, y abarca desde procedimientos modestos hasta otros más extensos.
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