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Abstract
Hilar cholangiocarcinoma, commonly known as Klatskin tumor, is a rare malignancy. Its etiopathogenesis is poorly understood but there is a strong association between chronic inflammation, cholestasis and cholangiocarcinoma. Known risk factors include primary sclerosing colangitis, fibrocystic liver disease, liver infections, hepatolithiasis, drugs and toxins. This tumor is characterized by presenting an asymptomatic clinical picture until advanced stages. Diagnosis is made by laboratory findings and diagnostic imaging. Treatment is based on surgery; there is no demonstrated evidence of a therapeutic benefit from radiation, chemotherapy, or a combination of both.
Keywords
References
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