Abstract
Aggressive angiomayxoma is a rare vulvar benign tumor first described by Steeper and Rosai in 1983. This tumor is a mesenchymal´s tumor that develops mainly in women’s pelvic and perineal región of women during the reproductive age. It is characterized by local recurrence and low ability to make distant metastases. Histologically, it has infiltrative borders, hypocellular, myxoid, with blood vessels of variable caliber and foci of hepatic extravasation
The cells are apparently fibroblastic with immunoreactivity for vimentin, desmin, actin and mainly for estrogen and progesterone receptors. The treatment is surgical, the roles of radiotherapy and hormonal treatment are not established yet.
Keywords
References
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